Influence of the use of hypercaloric oral nutritional supplement on the quality of life in children and adolescents with cystic fibrosis
DOI:
https://doi.org/10.12957/demetra.2025.74356Keywords:
Cystic fibrosis. Nutritional supplements. Quality of life.Abstract
Introduction: Cystic fibrosis (CF) is a chronic, genetic, and progressive disease, and early diagnosis and treatment developments have increased life expectancy. Objective: To evaluate the influence of high-calorie oral nutritional supplements on the quality of life (QoL) of children and adolescents with CF treated at a referral hospital in southern Brazil. Methods: This was a cross-sectional study of CF patients aged 2 to 14 years. Sociodemographic data, clinical characteristics, high-caloric oral nutritional supplement use, and QoL were reviewed using the Cystic Fibrosis Questionnaire (versions for children aged 6 to 11 years, 12 to 13 years, and ≥14 years) and the Pediatric Quality of Life Inventory (versions for children aged 2 to 4 years and 5 to 7 years). Study participants were categorized according to the age range of the relevant questionnaires. Results: Eighty-two patients participated in the study, of whom 73.2% used nutritional supplements. When comparing nutritional supplement use with QoL, children aged 2 to 4 years who used supplements had higher scores in the emotional domain. Among those aged 6 to 11 years, those who did not use nutritional supplements had higher scores in the physical domains: "body image," "food," "treatment," and "weight." Among 14-year-old adolescents, those using nutritional supplements exhibited lower scores in the "treatment" domain and higher scores in the "vitality" domain. Conclusion: The results of this study indicate that nutritional supplement use can influence different dimensions of QoL in different age groups.
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Copyright (c) 2025 Bruna Becker da Silva, Monica Ribeiro de Moraes, Aline Daiane Schlindwein, Betine Pinto Moehlecke Iser
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